兔抗clcn7多---抗体

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round:

the product of this gene belongs to the clc chloride channel family of proteins. chloride channels play important roles in the plasma membrane&in intracellular organelles. this gene encodes chloride channel 7. defects in this gene are the cause of osteopetrosis autosomal recessive type 4 (optb4), also called infantile malignant osteopetrosis type 2 as well as the cause of autosomal dominant osteopetrosis type 2 (opta2), also called autosomal dominant albers-schonberg disease/marble disease autosoml dominant. osteopetrosis is a rare genetic disease characterized by abnormally dense bone, due to defective resorption of immature bone. opta2 is the most common form of osteopetrosis, occurring in

applications:

elisa, wb

name of antibody:

clcn7

immunogen:

fusion protein of human clcn7

full name:

chloride voltage-gated channel 7

synonyms:

clc7; clc-7; opta2; optb4; ppp1r63

swissprot:

p51798

elisa recommended dilution:

5000-10000

wb predicted band size:

89 kda

wb positive control:

lovo&a549 cell, mouse liver tissue&rat liver tissue lysates

wb recommended dilution:

200-1000